WebApr 20, 2024 · Background Idiopathic non-specific interstitial pneumonia (iNSIP), idiopathic pleuroparenchymal fibroelastosis (iPPFE), and unclassifiable idiopathic interstitial pneumonia (IIP) are IIPs with chronic fibrotic phenotypes, and unlike idiopathic pulmonary fibrosis, they have often been treated with anti-inflammatory drugs, including … WebDec 1, 2011 · Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a recently described clinical-pathologic entity characterized by pleural and subpleural parenchymal fibrosis, …

High resolution CT and histological findings in idiopathic ...

WebJul 7, 2016 · Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare disease, idiopathic in most of the cases described in the literature. We report the case of a 55-year-old patient, non-smoker with tuberculosis treated in his youth, starting with progressive dyspnoea and cough, with radiographic abnormalities consisting of pleural thickening, … WebJennifer Fife, MD. Jennifer Fife, MD is a board-certified diagnostic radiologist with Spectrum Healthcare Partners. Dr. Fife provides professional physician services at RAYUS … passenger compartment air filter cf185

Idiopathic Pleuroparenchymal Fibroelastosis as a Rare Entity …

Pleuroparenchymal fibroelastosis (PPFE) is a rare, benign entity. About half of cases are felt to be idiopathic, with the other half secondary to underlying diseases or conditions (e.g. transplantation). Idiopathic cases belong to the group of idiopathic interstitial pneumonias. Epidemiology See more Pleuroparenchymal fibroelastosis is considered a rare disorder; however, it is very likely both under-recognized and misdiagnosed … See more The pathophysiology is unknown. Pleuroparenchymal fibroelastosis is characterized by predominantly upper … See more Most often significant chronic respiratory symptoms, which may include: 1. non-productive cough 2. dyspnea, either on exertion or in a worsening course 3. angina 4. frequent … See more Chest radiographs may be normal or present non-specific findings comprising: 1. marked bilateral apical pleural thickening 2. … See more WebIPPFE is defined histologically by coexisting upper lobe pleural and intra-alveolar fibrosis with elastosis. Dense subpleural irregular fibrosis and consolidation are the cardinal radiologic features. A history of recurrent lower respiratory tract infection is frequent. WebPleuroparenchymal fibroelastosis (PPFE) is an unusual pulmonary disease with unique clinical, radiological, and pathological characteristics. Designated a rare idiopathic … passenger company